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Classical
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Type I (gravis)
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43% of all cases
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Show all EDS features including mitral valve prolapse
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Type II (mitis)
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34% of all cases
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Mild but similar to type I
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Hypermobility
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Type III
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10% of all cases
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Skin unaffected
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Extensive hypermobility of joints
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Vascular
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Type IV
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6% of all cases
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Skin is noticeably translucent with visible veins but is not elastic
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Joints are unaffected
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Complications common and sudden death may occur at any time from large vessel rupture
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Kyphoscoliosis or ocular
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Type VI
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2% of all cases
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Eye involvement
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Scoliosis common (curved spine)
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Arthrochalasia
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Type VII A and B
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3% of all cases
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Noticeable joint hypermobility but less skin involvement
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Spontaneous joint dislocation common
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Dermatosparaxis
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Type VII C
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Other
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Type V
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5%
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Extensive skin hyperelasticity with splitting, bruising and scarring
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Type VIII (periodontal)
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Hyperelastic fragile skin
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Severe periodontitis (gum disease)
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Type IX
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Skeletal defects, characteristic bony horn-like overgrowths on back part of the skull
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Type X (fibronectin deficiency)
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Both rare
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These 2 types are so similar that they possibly should be classified together
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Type XI (benign hypermobile joint syndrome)
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